Online ISSN: 3007-0244,
Print ISSN:  2410-4280
EXPERIENCE IN IMPROVING SURGICAL TREATMENT WHEN IMPOSING A STOMA IN CHILDREN WITH HIRSPRUNG'S DISEASE
Hirpsprung's disease most often manifests as symptoms of intestinal obstruction, characterized by the colon nervous system congenital disability, frequent bloating, and impaired stool passage up to the clinic of intestinal obstruction. In recent years, this pathology has belonged to the group of neuro-crystopathy. The leading cause of death is the development of severe enterocolitis. Due to the lack of clear clinical manifestations, it is often observed that this disease goes undetected during the neonatal period. Currently, the only treatment is surgery. The final diagnosis is made after examining histopathological specimens, the diagnosis of which is difficult due to incomplete differentiation of the mucous and intermuscular layers in infancy.
Kanat S. Ashirbay1,2, https://orcid.org/0000-0002-0297-0364 Aueshan T. Jumabekov 2, https://orcid.org/0000-0002-3502-4411 Abay Z. Kussainov1,3, https://orcid.org/0000-0002-6256-7438 Gulmira B. Altynbayeva1,3, https://orcid.org/0000-0003-2178-3713 Кulyash К. Jaxalykova4, https://orcid.org/0000-0001-5540-3331 Konstantin E. Khairov1, https://orcid.org/0000-0002-0297-0364 Elmira B. Aitbayeva5, https://orcid.org/0000-0001-6434-0061 Nyshanbek R. Shilanbayev1, https://orcid.org/0000-0003-2572-7217 Medet Zhaksylyk1, https://orcid.org/0009-0008-4636-0630 1 JSC “Scientific Center of Pediatrics and Pediatric Surgery”, Almaty, Republic of Kazakhstan; 2 Kazakhstan Medical University “VSHOZ”, Almaty, Republic of Kazakhstan; 3 NJSC «Kazakh National Medical University named after S.D. Asfendiyarov», Almaty, Republic of Kazakhstan; 4 NJSC "Astana Medical University" Astana, Republic of Kazakhstan; 5 NJSC «Al-Farabi Kazakh National University», Almaty, Republic of Kazakhstan.
1. Говорухина О.А. Причины развития послеоперационного энтероколита при болезни Гиршпрунга у пациентов детского возраста // Новости хирургии. 2019. Т.27, №4. С. 421-427. https://dx.doi.org/10.18484/2305-0047.2019.4.369 (Дата обращения 10.01.2024) 2. Джорджесон К., Мюнстерер О., Мокрушина О.Г. Болезнь Гиршпрунга. В кн.: Непроходимость желудочно-кишечного тракта у детей. Национальное руководство / под ред. Козлова Ю.А., Подкаменева В.В., Новожилова В.А. - М.: ГЭОТАР-Медиа, 2017. – 446 c. https://www.geotar.ru/lots/NF0006695.html (Дата обращения 12.01.2024) 3. Каган А.В., Котин А.Н., Караваева С.А., Кесаева Т.В. Проблемы диагностики болезни Гиршпрунга у новорожденных: клинические примеры // Педиатр. 2020. Т.11. №1. С. 83-90. https://doi.org/10.17816/PED11183-90 (Дата обращения 23.01.2024) 4 Морозов Д.А., Пименова Е.С., Королев Г.А. Энтероколит у детей с болезнью Гиршпрунга // Биомед. Социол. 2018. Т.3, №4. С.103-107. http://dx.doi.org/10.26787/nydha-2618-8783-2018-3-4-103-107 (Дата обращения 14.01.2024г) 5. Alexandrescu S., Rosenberg H., Tatevian N. Role of calretinin immunohistochemical stain in evaluation of Hirschsprung disease: an institutional experience // Int. J. Clin. Exp. Pathol. 2013. Vol. 6(12). P. 2955-2961. www.ijcep.com/ISSN:1936-2625/IJCEP1310037 (Дата обращения 10.01.2024г) 6. Amiel J., Sproat-Emison E., Garcia-Barcelo M., Lantieri F., Burzynski G., Borrego S., Pelet А., Arnold S. et al. Hirschsprung disease, associated syndromes and genetics: a review // J. Med. Genet. 2008. Vol. 45. P.1-14. http://doi.org/10.1136/jmg.2007.053959 (accessed 10.01.2024) 7. Barshack I., Fridman E., Goldberg I., Chowers Y., Kopolovic J. The loss of calretinin expression indicates aganglionosis in Hirschsprung's disease // J. Clin. Pathol. 2004. Vol. 57. P. 712–716. http://dx.doi.org/10.1136/jcp.2004.016030 (accessed 08.01.2024) 8. Chakravarti A., McCallion A.S., Lyonnet S., Valle D.L., Antonarakis S., Ballabio A., Beaudet A.L., Mitchell G.A. et al. Hirschsprung Disease. Metabolic and Molecular Bases of Inherited Disease. New York: McGraw Hill, 2019. https://ommbid.mhmedical.com/content.aspx?bookid=2709§ionid=225899656 (accessed 11.01.2024) 9. Heuckeroth R. Hirschsprung disease – integrating basic science and clinical medicine to improve outcomes // Nat Rev Gastroenterol Hepatol. 2018. Vol.15. P.152–167. https://doi.org/10.1038/nrgastro.2017.149 (accessed 15.01.2024) 10. Kumari M., Das Ch., Mukhopadhyay M., Dev Patra R., Kumar Mitra P., Mukhopadhya B. A Study on Genetic Polymorphism of RET Proto-Oncogene in Hirschsprung’s Disease in Children // Afr. J. Paediatr. Surg. 2020. Vol. 17. P. 104-107. https://doi.org/10.4103/ajps.ajps_69_17 (accessed 20.01.204) 11. Langer J.C., Rollins M.D., Levitt M., Gosain A., L de la Torre, Kapur R.P., Cowles R.A. et al. Guidelines for the management of postoperative obstructive symptoms in children with Hirschsprung disease // Pediatr. Surg. Int. 2017. Vol. 33. P. 523-526. https://doi.org/10.1007/s00383-017-4066-7 (accessed 21.01.2024) 10. Lorijn F., Boeckxstaens G.E, Benninga M.A. Symptomatology, pathophysiology, diagnostic work-up, and treatment of Hirschsprung disease in infancy and childhood // Gastroenterolgy. Rep. 2007. Vol 9(3). P. 245-253. https://doi.org/10.1007/s11894-007-0026-z (accessed 20.01.2024) References: [1-4] 1. Govorukhina O.A. Prichiny razvitiya posleoperatsionnogo enterokolita pri bolezni Girshprunga u patsientov detskogo vozrasta [Causes of development of postoperative enterocolitis in Hirschsprung's disease in pediatric]. Novosti khirurgii [Surgery news.]. 2019. T.27, №4. рр. 421-427 https://dx.doi.org/10.18484/2305-0047.2019.4.369 (accessed 10.01.2024) [in Russian] 2. Dzhordzheson K., Myunsterer O., Mokrushina O.G., Kozlov Yu.A., Podkamenev V.V., Novozhilov V.A. Bolezn' Girshprunga. V kn.: Neprokhodimost' zheludochno-kishechnogo trakta u detei. Natsional'noe rukovodstvo [Hirschsprung's disease. In the book: Obstruction of the gastrointestinal tract in children. National leadership].- M.: GEOTAR-Media, 2017. – 446p. https://www.geotar.ru/lots/NF0006695.html (accessed 12.01.2024) [in Russian] 3. Kagan A.V., Kotin A.N., Karavaeva S.A., Kesaeva T.V. Problemy diagnostiki bolezni Girshprunga u novorozhdennykh: klinicheskie primery [Problems in diagnosing Hirschsprung's disease in newborns: clinical examples]. Pediatr [Pediatrician]. 2020. T.11. №1. pp. 83-90. https://doi.org/10.17816/PED11183-90 (accessed 13.01.2024) [in Russian] 4 Morozov D.A., Pimenova E.S., Korolev G.A. Enterokolit u detei s bolezn'yu Girshprunga Enterocolitis in children with Hirschsprung disease]. Biomed. Sotsiol. [Bulletin "Biomedicine and sociology"]. 2018. T.3, №4. pp.103-107. http://dx.doi.org/10.26787/nydha-2618-8783-2018-3-4-103-107 (accessed 14.01.2024) [in Russian]
Number of Views: 72


Category of articles: Original articles

Bibliography link

Ashirbay K.S., Jumabekov A.T., Kussainov A.Z., Altynbayeva G.B., Jaxalykova К.К., Khairov K.E., Aitbayeva E.B., Shilanbayev N.R., Zhaksylyk M. Experience in improving surgical treatment when imposing a stoma in children with Hirsprung's disease // Nauka i Zdravookhranenie [Science & Healthcare]. 2024. Т.26 (2), pp. 82-88. doi 10.34689/SH.2024.26.2.011

Авторизируйтесь для отправки комментариев