EXPERIENCE IN IMPROVING SURGICAL TREATMENT WHEN IMPOSING A STOMA IN CHILDREN WITH HIRSPRUNG'S DISEASE
Hirpsprung's disease most often manifests as symptoms of intestinal obstruction, characterized by the colon nervous system congenital disability, frequent bloating, and impaired stool passage up to the clinic of intestinal obstruction. In recent years, this pathology has belonged to the group of neuro-crystopathy. The leading cause of death is the development of severe enterocolitis. Due to the lack of clear clinical manifestations, it is often observed that this disease goes undetected during the neonatal period. Currently, the only treatment is surgery. The final diagnosis is made after examining histopathological specimens, the diagnosis of which is difficult due to incomplete differentiation of the mucous and intermuscular layers in infancy.
Kanat S. Ashirbay1,2, https://orcid.org/0000-0002-0297-0364
Aueshan T. Jumabekov 2, https://orcid.org/0000-0002-3502-4411
Abay Z. Kussainov1,3, https://orcid.org/0000-0002-6256-7438
Gulmira B. Altynbayeva1,3, https://orcid.org/0000-0003-2178-3713
Кulyash К. Jaxalykova4, https://orcid.org/0000-0001-5540-3331
Konstantin E. Khairov1, https://orcid.org/0000-0002-0297-0364
Elmira B. Aitbayeva5, https://orcid.org/0000-0001-6434-0061
Nyshanbek R. Shilanbayev1, https://orcid.org/0000-0003-2572-7217
Medet Zhaksylyk1, https://orcid.org/0009-0008-4636-0630
1 JSC “Scientific Center of Pediatrics and Pediatric Surgery”, Almaty, Republic of Kazakhstan;
2 Kazakhstan Medical University “VSHOZ”, Almaty, Republic of Kazakhstan;
3 NJSC «Kazakh National Medical University named after S.D. Asfendiyarov», Almaty, Republic of Kazakhstan;
4 NJSC "Astana Medical University" Astana, Republic of Kazakhstan;
5 NJSC «Al-Farabi Kazakh National University», Almaty, Republic of Kazakhstan.
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Ashirbay K.S., Jumabekov A.T., Kussainov A.Z., Altynbayeva G.B., Jaxalykova К.К., Khairov K.E., Aitbayeva E.B., Shilanbayev N.R., Zhaksylyk M. Experience in improving surgical treatment when imposing a stoma in children with Hirsprung's disease // Nauka i Zdravookhranenie [Science & Healthcare]. 2024. Т.26 (2), pp. 82-88. doi 10.34689/SH.2024.26.2.011Related publications:
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EXPERIENCE IN IMPROVING SURGICAL TREATMENT WHEN IMPOSING A STOMA IN CHILDREN WITH HIRSPRUNG'S DISEASE